Status | Study |
Recruiting |
Study Name: Nitric Oxide Supplementation on Neurocognitive Functions in Patients With ASLD Condition: Argininosuccinate Lyase Deficiency Urea Cycle Disorder Date: 2017-02-10 Interventions: Dietary Supplement: Neo-ASA Di |
Not yet recruiting |
Study Name: Urease Inhibitor Drug Treatment for Urea Cycle Disorders Condition: Ornithine Transcarbamylase Deficiency Argininosuccinate Synthetase Deficiency (Citrullinemia Date: 2016-01-14 Interventions: Drug: Acetohydroxamic Acid Oth |
Recruiting |
Study Name: Nitric Oxide Supplementation in Argininosuccinic Aciduria Condition: Argininosuccinic Aciduria Argininosuccina Date: 2014-09-25 Interventions: Dietary Supplement: Nitric oxide supplement |
Completed |
Study Name: Pilot Study For Hypothermia Treatment In Hyperammonemic Encephalopathy In Neonates And Very Young Infants Condition: Urea Cycle Disorders Organic Acidemias Date: 2012-06-13 Interventions: Other: Therapeutic Hypothermia |
Terminated |
Study Name: The NIH UNI Study: Urea Cycle Disorders, Nutrition and Immunity Condition: Argininosuccinic Aciduria Carbamoyl-Phosphate Synthase I Defici Date: 2011-08-20 |
Completed |
Study Name: Arginine and Buphenyl in Patients With Argininosuccinic Aciduria (ASA), a Urea Cycle Disorder Condition: Argininosuccinic Aciduria Amino Acid Metabolism, Inborn Errors Date: 2006-06-26 Interventions: Drug: Sodium Phenylbutyrate No |