Status | Study |
Recruiting |
Study Name: Safety, Tolerability, and Immunogenicity of One Dose of NDV 3A Vaccine in People With STAT3-Mutated Hyper-IgE Syndrome Condition: Autosomal-dominant Hyper-IgE Syndrome Date: 2016-12-16 Interventions: Drug: NDV-3A A vaccine containing recombinant Candida albicans agglutinin-like sequence 3 (rAls3) protei |
Recruiting |
Study Name: CAMB/MAT2203 in Patients With Mucocutaneous Candidiasis Condition: Candidiasis, Chronic Mucocutaneous Date: 2015-11-16 Interventions: Drug: Amphotericin B Lipid crystal nano-particle formulation of amphotericin B |
Recruiting |
Study Name: NFIL3-induced Pathological Enhancement of IgE Class Switch Recombination in Hyper-IgE Syndrome Condition: Job Syndrome Date: 2014-08-18 |
Recruiting |
Study Name: Sequential Cadaveric Lung and Bone Marrow Transplant for Immune Deficiency Diseases Condition: Severe Combined Immunodeficiency (SCID) Immunodeficiency With Predominant T-cell Defect, Uns Date: 2013-04-26 Interventions: Biological: CD3/CD19 negative allogeneic hematopoietic stem cells Negative selection for CD3/CD19 will b |
Terminated |
Study Name: Effect of Ranitidine on Hyper-IgE Recurrent Infection (Job's) Syndrome Condition: JOB's Syndrome Hyper-IgE Recurrent Infection Syndrome Date: 2007-09-08 Interventions: Drug: Ranitidine Double blinde |
Recruiting |
Study Name: Collection of Lung Fluid and Tissue Samples for Research Condition: Mycobacterium Infections, Atypical Granulomatous Disease, Chronic Date: 2007-05-08 |
Recruiting |
Study Name: Detection and Characterization of Infections and Infection Susceptibility Condition: Immune Disorders Chronic Granulomatous Disease Genetic Imm Date: 2006-11-28 |
Completed |
Study Name: Omalizumab to Treat Hyper-IgE (Job's) Syndrome Condition: Hyper-IgE Syndrome Job's Syndrome Date: 2005-12-01 Interventions: Drug: Omalizumab (Xolair) |
Completed |
Study Name: Posaconazole to Treat Invasive Fungal Infections Condition: Granulomatous Disease, Chronic Job's Syndrome Date: 2002-04-18 Interventions: Drug: Posaconazole |
Recruiting |
Study Name: Study of Mycobacterial Infections Condition: Atypical Mycobacterium Infections Cystic Fibrosis Date: 2001-06-28 |